THE IMPLICATIONS OF MULTIPLE FORMS OF PHENYLALANINE HYDROXYLASE IN PHENYLKETONURIA AND RELATED DISEASES OF PHENYLALANINE METABOLISM.BARRANGER JA.1976; BIOCHEM. MED.; U.S.A.; DA. 1976; VOL. 15; NO 1; PP. 55-86; BIBL. 4 P. 1/2Article

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